A Chiari malformation, previously called an Arnold-Chiari malformation, is where the lower part of the brain pushes down into the spinal canal.
There are 4 main types, but type 1, called Chiari I, is the most common.
In someone with Chiari I, the lowest part of the back of the brain extends into the spinal canal. This can put pressure on the brainstem, spinal cord, and obstruct the flow of fluid.
This page focuses on Chiari I malformations.
The severity of Chiari malformations can vary from person to person, but generally:
Talk to your doctor about what the condition means, what the implications may be for your health and what treatment you may need.
Many people with a Chiari I malformation will not have any symptoms. Sometimes they're only found after an (MRI) scan of the brain is carried out for another reason.
If symptoms do develop, they can include:
If you develop syringomyelia, you may also experience problems using your hands, difficulty walking, pain, and problems with bladder or bowel control.
If you've been diagnosed with a Chiari malformation, you should contact your doctor for advice if you develop any new symptoms or your symptoms worsen.
Treatment for Chiari I malformation depends on whether you have any symptoms and how severe they are. You might not need any treatment if you do not have any symptoms.
Painkillers can help relieve any headaches and neck pain.
If your headaches are severe or you have problems caused by the pressure on your spinal cord (such as movement difficulties), surgery may be recommended.
The main operation for Chiari malformation is called decompression surgery.
Under general anaesthetic a cut is made at the back of your head and the surgeon removes a small piece of bone from the base of your skull. They may also remove a small piece of bone from the top of your spine.
This will help reduce the pressure on your brain and allow the fluid in and around your brain and spinal cord to flow normally. Read an NHS leaflet about decompression for Chiari malformation (PDF, 111kb).
Other procedures that may be necessary include:
The aim of surgery is to stop existing symptoms getting any worse. Some people also experience an improvement in their symptoms, particularly their headaches.
Talk to your surgeon about the different surgical options and what the benefits and risks of each are.
The exact cause of Chiari I malformations is unknown. It tends to be present from birth, but is normally only found in adulthood when symptoms develop or when an MRI scan is done.
Many cases are thought to be the result of part of the skull not being large enough for the brain.
Chiari I malformations can also develop in people with a tethered spinal cord, a build-up of fluid on the brain (hydrocephalus), and some types of brain tumour.
Chiari malformations can sometimes run in families. It's possible that some children born with it may have inherited a faulty gene that caused problems with their skull development.
But the risk of passing a Chiari malformation on to your child is very small. And remember: even if your children do inherit it, they may not experience symptoms.
If you have been affected by a Chiari malformation, your clinical team will pass information about you on to the National Congenital Anomaly and Rare Diseases Registration Service (NCARDRS).
This helps scientists look for better ways to prevent and treat this condition. You can opt out of the register at any time.