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Diagnosis

Idiopathic pulmonary fibrosis (IPF) can be hard to diagnose because its symptoms are similar to other lung conditions, such as chronic obstructive pulmonary disease (COPD).

A GP can refer you to hospital specialists for a number of tests to help rule out other conditions and confirm the diagnosis.

Medical history and examination

Your doctor will ask about your medical history and whether there are other factors that could be causing a problem with your lungs, such as whether you:

They may also:

Breathing and blood tests

Lung function tests (also called pulmonary function tests) assess how well your lungs work and can help indicate what the problem may be.

These tests measure:

A commonly used lung function test is spirometry. During the test, you breathe into a mouthpiece that's attached to a monitor.

Chest X-ray and CT scan

A chest X-ray does not show the lungs in much detail, but can help doctors spot some more obvious problems that could be causing your symptoms, such as cancer or a build-up of fluid.

If IPF is suspected, the chest X-ray will be followed by a CT scan.

A CT scan is similar to an X-ray, but lots more images are taken and these are put together by a computer to create a more detailed image of your lungs.

This can help your doctor spot signs of scarring in your lungs.

Bronchoscopy

If doctors are still not sure what the problem is after these tests, they may suggest having a bronchoscopy.

This is a test where a narrow, flexible tube with a camera (bronchoscope) is passed down into your airways.

Your doctor will look for anything abnormal and may take small tissue samples for testing.

You'll usually be awake during a bronchoscopy and it may cause coughing.

Local anaesthetic will be used to numb your throat so it does not hurt, and you may also be given a sedative injection that'll make you feel sleepy during the procedure.

Lung biopsy

If other tests are not conclusive, a lung biopsy may need to be carried out.

This involves keyhole surgery to remove a small sample of lung tissue so it can be analysed for signs of scarring.

This is performed under a general anaesthetic, where you're asleep. 

Your surgeon makes several small cuts in your side and an endoscope, a thin tube with a camera and a light at the end, is inserted into the area between the lungs and the chest wall.

The surgeon can see the lung tissue through the endoscope and is able to obtain a small sample.